Article
Alpha-1 antitrypsin deficiency panniculitis: clinical and pathologic characteristics of 10 cases.
International journal of dermatology - 1 Aug 2018
Johnson Emma F, Tolkachjov Stanislav N, Gibson Lawrence E
Abstract excerpt
BACKGROUND: Alpha-1 antitrypsin deficiency (AATD) may be associated with liver and lung disease and rarely causes panniculitis. OBJECTIVE: We evaluated the clinicopathologic and laboratory findings of AATD panniculitis in 10 patients. METHODS: We conducted a retrospective review of all cases of AATD panniculitis at Mayo Clinic, Rochester, MN, from 1989 to 2016. RESULTS: Ten patients with AATD panniculitis were...
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