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Article

Evaluation of families wherein a single male manifests a phenotype of X-linked lymphoproliferative disease (XLP).

American journal of medical genetics - 15 Sept 1993

Grierson H L, Skare J, Church J, Silberman T, Davis J R, Kobrinsky N, McGregor R, Israels S, McCarty J, Andrews L G

Abstract excerpt

The Epstein-Barr virus (EBV)-induced diseases of males with X-linked lymphoproliferative disease (XLP) include fatal infectious mononucleosis (IM), non-Hodgkin lymphoma (ML), agammaglobulinemia, and aplastic anemia. These phenotypes also occur as sporadic cases in families, and EBV seronegative males in these families must be considered at risk for XLP until they seroconvert normally to EBV. Given that 50% of...

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Identifiers

PMID: 8256804
DOI: 10.1002/ajmg.1320470404

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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Evaluation of families wherein a single male manifests a phenotype of X-linked lymphoproliferative disease (XLP).PMID 8256804Read ↗

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