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Article

Utilising human cellular models of primary ciliary dyskinesia: a scoping review.

European respiratory review : an official journal of the European Respiratory Society - 1 Jul 2026

Ong Jonathan W Y, Tsang William, Lucas Jane S, Jackson Claire L, Rubbo Bruna

Abstract excerpt

BACKGROUND: Primary ciliary dyskinesia (PCD) comprises a group of rare genetic disorders that primarily affect the function of motile respiratory cilia, leading to progressive sinopulmonary disease. Disease models can be used to investigate potential therapies or responses to environmental exposures. We sought to identify and describe knowledge gaps in the modelling approaches and outcome measures used in applied...

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Identifiers

PMID: 42386308
DOI: 10.1183/16000617.0193-2025
PMCID: PMC13320618

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026.

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