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Article

Angiomyolipoma/PEComa: the past, the present…and back to the future.

Current opinion in urology - 1 Mar 2026

Caliò Anna, Marletta Stefano, Martignoni Guido

Abstract excerpt

PURPOSE OF REVIEW: This review provides a comprehensive update on renal angiomyolipoma, a mesenchymal neoplasm within the PEComa family. It revisits its historical classification, evolving pathological understanding, and recent molecular insights, emphasizing its relevance in current diagnostic and pathogenetic contexts. RECENT FINDINGS: Angiomyolipoma/PEComa has transitioned from being considered a hamartoma to...

Topics

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Biomarkers, Tumor
Diagnosis, Differential
TSC1 gene
TSC2 gene
Kidney Neoplasms
Mutation

Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

Signal Transduction

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Identifiers

PMID: 41373175
DOI: 10.1097/MOU.0000000000001362

Genes

TFEB
GPNMB
TRIM63
TSC1
TSC2

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 1 Sept 2026.

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