Article
Real-World Evidence on the Management of Hereditary Angioedema With Normal C1 Inhibitor.
The journal of allergy and clinical immunology. In practice - 1 Jan 2026
Lobão Nyla Thyara Melo, Bardou Maine Luellah Demaret, Vila Shirley Yajaira Cerinza, Sousa Ferreira Lucas Salomão de, Arruda Luisa Karla, Lemos José Eduardo Seneda, Ferriani Mariana Paes Leme, Dias Marina Mendonça, Toledo Eliana Cristina, Serpa Faradiba Sarquis, Moyses Therezinha Ribeiro, Chong-Neto Herberto J, Rosário Filho Nelson Augusto, de Moraes Caroline Guth de Freitas Batista, Marcelino Fernanda Casares, Mansour Eli, Coutinho Caroline Rosa Emergente, Mendes Ronney Corrêa, Gonçalves Rozana de Fátima, Valle Solange Oliveira Rodrigues, Oliva-Alonso Maria Luiza, Dortas Junior Sérgio Duarte, da Silva Jane, de Souza Aline Lara Fonseca, Ensina Luis Felipe, Morato Vanessa, de Albuquerque Campos Regis, Pesquero João Bosco, Constantino-Silva Rosemeire Navickas, Grumach Anete Sevciovic
Abstract excerpt
BACKGROUND: Hereditary angioedema (HAE) with normal C1 inhibitor (HAE-nC1INH) is a rare and heterogeneous group of bradykinin-mediated disorders, characterized by diagnostic challenges and limited evidence-based recommendations. OBJECTIVE: To describe the clinical features and therapeutic strategies of Brazilian patients with HAE-nC1INH, supporting individualized, subtype-oriented management. METHODS: This...
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