Article
Sarcomere gene variants did not improve cardiac function in pediatric patients with dilated cardiomyopathy from Japanese cohorts.
Scientific reports - 16 Dec 2024
Hirono Keiichi, Hata Yukiko, Ichimata Shojiro, Nishida Naoki, Imamura Teruhiko, Asano Yoshihiro, Kuramoto Yuki, Tsuboi Kaori, Takarada Shinya, Okabe Mako, Nakaoka Hideyuki, Ibuki Keijiro, Ozawa Sayaka, Muneuchi Jun, Yasuda Kazushi, Urayama Kotaro, Oka Hideharu, Miyamoto Tomoyuki, Baba Kenji, Kato Akio, Saiki Hirofumi, Kuwabara Naoki, Harada Masako, Baba Shiro, Morikawa Mari, Iwasaki Hidenori, Hirata Yuichiro, Ito Yuki, Sakaguchi Heima, Urata Susumu, Toda Koichi, Kittaka Emi, Okada Seigo, Hasebe Yohei, Hoshino Shinsuke, Fujii Takanari, Mitsushita Norie, Nii Masaki, Ogino Kayo, Fujino Mitsuhiro, Yoshida Yoko, Fukuda Yutaka, Iwashima Satoru, Takigiku Kiyohiro, Sakata Yasushi, Inuzuka Ryo, Maeda Jun, Hayabuchi Yasunobu, Fujioka Tao, Namiki Hidemasa, Fujita Shuhei, Nishida Koichi, Kuraoka Ayako, Kan Nobuhiko, Kido Sachiko, Watanabe Ken, Ichida Fukiko
Abstract excerpt
Dilated cardiomyopathy (DCM) is a progressive myocardial disorder characterized by impaired cardiac contraction and ventricular dilation. However, some patients with DCM improve when experiencing left ventricular reverse remodeling (LVRR). Currently, the detailed association between genotypes and clinical outcomes, including LVRR, particularly among children, remains uncertain. Pediatric patients with DCM from...
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