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Article

Cutaneous findings and treatment responses of lipoid proteinosis patients.

International journal of dermatology - 1 Jan 2025

An İsa

Abstract excerpt

OBJECTIVES: Lipoid proteinosis (LP) is a rare autosomal recessive disorder characterized by the accumulation of hyaline-like material in the skin, oral mucosa, larynx, and brain. This study aimed to evaluate the dermatological findings and treatment responses of patients diagnosed with LP. METHODS: This retrospective study included 41 patients diagnosed with LP at our clinic between May 2018 and January 2023. The...

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PMID: 38876475
DOI: 10.1111/ijd.17331

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