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Article

Pulmonary Vascular Dysfunctions in Cystic Fibrosis.

Physiology (Bethesda, Md.) - 1 Jul 2024

Amoakon Jean-Pierre, Mylavarapu Goutham, Amin Raouf S, Naren Anjaparavanda P

Abstract excerpt

Cystic fibrosis (CF) is an inherited disorder caused by a deleterious mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene. Given that the CFTR protein is a chloride channel expressed on a variety of cells throughout the human body, mutations in this gene impact several organs, particularly the lungs. For this very reason, research regarding CF disease and CFTR function has historically...

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Source

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Identifiers

PMID: 38501963
DOI: 10.1152/physiol.00024.2023
PMCID: PMC11368519

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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