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Article

Clinical phenotypes and long-term outcome of kidney involvement in Erdheim-Chester histiocytosis.

Kidney international - 1 Jan 2023

Chazal Thibaud, Pegoraro Francesco, Manari Gaia, Bettiol Alessandra, Maniscalco Valerio, Gelain Elena, Charlotte Frédéric, Mazor Roei D, Renard-Penna Raphaele, Amoura Zahir, Cohen-Aubart Fleur, Haroche Julien, Izzedine Hassan, Vaglio Augusto

Abstract excerpt

Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis that frequently infiltrates the peri-kidney space ("hairy kidney" appearance), kidney pelvis and proximal ureters, leading to obstructive uropathy. Here, we analyzed the clinical characteristics, imaging findings and long-term kidney outcome of a large multicenter cohort comprising 195 consecutive patients with ECD. Retroperitoneal...

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Identifiers

PMID: 36374823
DOI: 10.1016/j.kint.2022.09.027

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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