Article
Pattern-based Histologic Approach in Very Early Onset IBD: Main Features and Differential Diagnosis.
Advances in anatomic pathology - 1 Mar 2022
Parente Paola, Mastracci Luca, Vanoli Alessandro, Fassan Matteo, Pastore Maria, Bossa Fabrizio, Francalanci Paola, Alaggio Rita, Graziano Paolo, Grillo Federica
Abstract excerpt
Very early onset inflammatory bowel disease (VEO-IBD) is a clinical umbrella classification composed of IBD-like diseases encompassing both classic IBD (Crohn's disease and ulcerative colitis) and monogenic disorder, both arising before 6 years of age. VEO-IBD patients present significant clinical differences from IBD occurring in older children and in adults, including more severe disease, often unresponsive to...
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