Article
Characteristics of thrombocytopenia, anasarca, fever, reticulin fibrosis and organomegaly syndrome: a retrospective study from a large Western cohort.
British journal of haematology - 1 Feb 2022
Maisonobe Lucas, Bertinchamp Rémi, Damian Louise, Gérard Laurence, Berisha Mirlinda, Guillet Stéphanie, Fieschi Claire, Malphettes Marion, Fadlallah Jehane, Hié Miguel, Dunogué Bertrand, De Wilde Virginie, Vandergheynst Frédéric, Zafrani Lara, Grall Maximilien, Saada Noémie, Garzaro Margaux, Oksenhendler Eric, Galicier Lionel, Boutboul David
Abstract excerpt
Idiopathic multicentric Castleman disease (iMCD) is a non-clonal inflammatory lymphoproliferative disorder of unknown origin. Recently, TAFRO syndrome (thrombocytopenia, anasarca, fever, reticulin fibrosis and organomegaly) emerged as a singular variant of iMCD in Asia and was associated with a severe course and a poor outcome. The present study describes the first large Western cohort of TAFRO syndrome patients...
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