Article
Overlapping forms of granulomatosis with polyangiitis and eosinophilic granulomatosis with polyangiitis: Insights from a European multicenter study.
Journal of internal medicine - 1 Mar 2026
Pallotti Federica, Mettler Camille, Papo Matthias, Iudici Michele, Padoan Roberto, Sorin Boris, Regola Francesca, Franceschini Franco, Moiseev Sergey, Novikov Pavel, Piga Mario Andrea, Moroncini Gianluca, Brix Silke R, Kafagi Abdul Hadi, Deshayes Samuel, Aouba Achille, Campagne Julien, Delvino Paolo, Tervaert Jan Willem Cohen, Brussino Luisa, Michaud Martin, Venhoff Nils, Alberici Federico, Iannone Claudia, Rosenstingl Sophie, Moutel Marin, Galempoix Jean-Marc, Cottin Vincent, Jaccard Clara, Riehl Diane, Legendre Paul, Billet Anne Claire, Parronchi Paola, Quartuccio Luca, Teixeira Vitor, Egan Allyson, Jayne David, Tombetti Enrico, Caminati Marco, Pagnoux Christian, Regent Alexis, Ruivard Marc, Guillevin Loïc, Puéchal Xavier, Terrier Benjamin
Abstract excerpt
BACKGROUND: Granulomatosis with polyangiitis (GPA) and eosinophilic granulomatosis with polyangiitis (EGPA) are distinct forms of antineutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV). Increasing evidence suggests overlapping features, particularly in proteinase 3 (PR3)-ANCA-positive EGPA and GPA with eosinophilia. This study aimed to characterize overlapping EGPA/GPA forms and assess their...
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