Article
Roles of Immune Cells in Hereditary Angioedema.
Clinical reviews in allergy & immunology - 1 Jun 2021
Ferrara Anne Lise, Cristinziano Leonardo, Petraroli Angelica, Bova Maria, Gigliotti Maria Celeste, Marcella Simone, Modestino Luca, Varricchi Gilda, Braile Mariantonia, Galdiero Maria Rosaria, Spadaro Giuseppe, Loffredo Stefania
Abstract excerpt
Hereditary angioedema (HAE) is a rare genetic disease, characterized by recurrent and unexpected potentially life-threatening mucosal swelling. HAE may be further classified into HAE with C1-inhibitor deficiency (C1-INH-HAE) and HAE with normal C1-INH activity (nlC1-INH-HAE), mostly due to mutations leading to increased vascular permeability. Recent evidence implicates also the innate and adaptive immune...
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