Article
Blastic Plasmacytoid Dendritic Cell Neoplasm in Children.
Hematology/oncology clinics of North America - 1 Jun 2020
Li Yixian, Sun Victoria, Sun Weili, Pawlowska Anna
Abstract excerpt
Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare, aggressive hematological malignancy, derived from plasmacytoid dendritic cells. It mainly occurs in older adults, but has been reported across all age groups. Most patients present with skin lesions with or without marrow involvement and leukemic dissemination. Treatment with high-risk acute lymphoblastic leukemia therapy regimens with central...
Topics
- Age Factors
- Biomarkers
- Child
- Combined Modality Therapy
- Dendritic Cells
- Diagnosis, Differential
- Disease Management
- Disease Susceptibility
- Humans
- Immunophenotyping
- Myeloproliferative Disorders
