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Article

Validation of the new classification criteria for hereditary recurrent fever in an independent cohort: experience from the JIR Cohort Database.

Rheumatology (Oxford, England) - 1 Oct 2020

Dingulu Glory, Georgin-Lavialle Sophie, Koné-Paut Isabelle, Pillet Pascal, Pagnier Anne, Merlin Etienne, Kaiser Daniela, Belot Alexandre, Hofer Michael, Hentgen Véronique

Abstract excerpt

OBJECTIVE: The new classification criteria for the hereditary recurrent fever (HRF) syndrome [cryopyrin-associated periodic syndrome (CAPS), TNF-α receptor-associated periodic syndrome (TRAPS), FMF and mevalonate kinase deficiency] have been published recently. These criteria define two core sets of criteria for each HRF: mixed criteria, including genetic and clinical variables, and clinical criteria, relying on...

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PMID: 32125423
DOI: 10.1093/rheumatology/keaa031

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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