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Article

T Cell Impairment Is Predictive for a Severe Clinical Course in NEMO Deficiency.

Journal of clinical immunology - 1 Apr 2020

Heller Stephanie, Kölsch Uwe, Magg Thomas, Krüger Renate, Scheuern Andrea, Schneider Holm, Eichinger Anna, Wahn Volker, Unterwalder Nadine, Lorenz Myriam, Schwarz Klaus, Meisel Christian, Schulz Ansgar, Hauck Fabian, von Bernuth Horst

Abstract excerpt

PURPOSE: NEMO-deficient patients present with variable degrees of immunodeficiency. Accordingly, treatment ranges from antibiotic prophylaxis and/or IgG-substitution to allogenic hematopoietic stem cell transplantation (HSCT). The correct estimation of the immunodeficiency is essential to avoid over- as well as under-treatment. We compare the immunological phenotype of a NEMO-deficient patient with a...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Source

Identifiers

PMID: 31965418
DOI: 10.1007/s10875-019-00728-y

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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T Cell Impairment Is Predictive for a Severe Clinical Course in NEMO Deficiency.PMID 31965418Read ↗

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