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Article

Molecular Pathogenesis of Familial Wolff-Parkinson-White Syndrome.

The journal of medical investigation : JMI - 1 Jan 2018

Miyamoto Licht

Abstract excerpt

Familial Wolff-Parkinson-White (WPW) syndrome is an autosomal dominant inherited disease and consists of a small percentage of WPW syndrome which exhibits ventricular pre-excitation by development of accessory atrioventricular pathway. A series of mutations in PRKAG2 gene encoding gamma2 subunit of 5'AMP-activated protein kinase (AMPK) has been identified as the cause of familial WPW syndrome. AMPK is one of the...

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Identifiers

PMID: 29593177
DOI: 10.2152/jmi.65.1

Genes

PRKAG2

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026.

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