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Article

Successful kidney transplantation in a patient with congenital thrombotic thrombocytopenic purpura (Upshaw-Schulman syndrome).

Transfusion - 1 Dec 2017

Fattah Hasan, Kumar Dhiren, George James N, Massey H Davis, King Anne L, Friedman Kenneth D, Gupta Gaurav

Abstract excerpt

BACKGROUND: Congenital thrombotic thrombocytopenic purpura (TTP) may not be recognized until organ failure related to the microvascular thrombosis occurs. Kidney failure may be the initial presenting clinical feature. Kidney transplantation has been contraindicated because of the assumption that the continuing microvascular thrombosis will cause inevitable graft failure. CASE REPORT: We report a 48-year-old...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Identifiers

PMID: 28940540
DOI: 10.1111/trf.14326

Genes

ADAMTS13

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 3 Sept 2026.

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