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Article

[Hereditary form of thrombotic thrombocytopenic purpura].

Casopis lekaru ceskych - 1 Jan 2006

Hrachovinová I, Rittich S, Salaj P, Suttnar J, Dyr J E, Suláková T, Pták J, Dulícek P, Seeman T

Abstract excerpt

BACKGROUND: Thrombotic thrombocytopenic purpura is characterized by microvascular platelet clumping resulting in thrombocytopenia, microangiopathic hemolysis, neurological abnormality, and renal dysfunction. Similar manifestations also occur in patients with the hemolytic uremic syndrome or other types of disorders. Recent studies demonstrate that severe deficiency of the von Willebrand factor cleaving...

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Identifiers

PMID: 16755777

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ADAMTS13

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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