Article
A current approach to heart failure in Duchenne muscular dystrophy.
Heart (British Cardiac Society) - 1 Nov 2017
D'Amario Domenico, Amodeo Antonio, Adorisio Rachele, Tiziano Francesco Danilo, Leone Antonio Maria, Perri Gianluigi, Bruno Piergiorgio, Massetti Massimo, Ferlini Alessandra, Pane Marika, Niccoli Giampaolo, Porto Italo, D'Angelo Gianluca A, Borovac Josip Anđelo, Mercuri Eugenio, Crea Filippo
Abstract excerpt
Duchenne muscular dystrophy (DMD) is a genetic, progressive neuromuscular condition that is marked by the long-term muscle deterioration with significant implications of pulmonary and cardiac dysfunction. As such, end-stage heart failure (HF) in DMD is increasingly becoming the main cause of death in this population. The early detection of cardiomyopathy is often challenging, due to a long subclinical phase of...
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