Article

Cardiac Involvement in Emery-Dreifuss Muscular Dystrophy: From Arrhythmias to Heart Failure and Sudden Death: A Contemporary Review

2026-03-27

Abstract excerpt

<h4>Background: </h4> Emery–Dreifuss muscular dystrophy (EDMD) is a rare inherited neuromuscular disorder within the spectrum of nuclear envelope diseases, classically characterized by early musculo-tendinous contractures, slowly progressive myopathy and cardiac involvement dominated by conduction disease and arrhythmias, with variable evolution toward cardiomyopathy and heart failure. <h4>Methods:</h4> We perform...

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Literature Corpus work: 15a794a2-9005-5754-b18f-faded5193e8c
DOI: 10.20944/preprints202603.2226.v1

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