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Article

Transmissibility of Gerstmann-Sträussler-Scheinker syndrome in rodent models: New insights into the molecular underpinnings of prion infectivity.

Prion - 1 Nov 2016

Nonno Romolo, Angelo Di Bari Michele, Agrimi Umberto, Pirisinu Laura

Abstract excerpt

Prion diseases, or transmissible spongiform encephalopathies, have revealed the bewildering phenomenon of transmissibility in neurodegenerative diseases. Hence, the experimental transmissibility of prion-like neurodegenerative diseases via template directed misfolding has become the focus of intense research. Gerstmann-Sträussler-Scheinker disease (GSS) is an inherited prion disease associated with mutations in...

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Identifiers

PMID: 27892798
DOI: 10.1080/19336896.2016.1239686
PMCID: PMC5161296

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GSS

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