Article
Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) Associated With Ryanodine Receptor (RyR2) Gene Mutations - Long-Term Prognosis After Initiation of Medical Treatment.
Circulation journal : official journal of the Japanese Circulation Society - 25 Aug 2016
Kawata Hiro, Ohno Seiko, Aiba Takeshi, Sakaguchi Heima, Miyazaki Aya, Sumitomo Naokata, Kamakura Tsukasa, Nakajima Ikutaro, Inoue Yuko Y, Miyamoto Koji, Okamura Hideo, Noda Takashi, Kusano Kengo, Kamakura Shiro, Miyamoto Yoshihiro, Shiraishi Isao, Horie Minoru, Shimizu Wataru
Abstract excerpt
BACKGROUND: The long-term prognosis of cardiac ryanodine receptor (RyR2) positive catecholaminergic polymorphic ventricular tachycardia (CPVT) patients after initiation of medical therapy has not been well investigated. This study aimed to assess the recurrence of fatal cardiac event after initiation of medical therapy inRyR2-positive CPVT patients. METHODS AND RESULTS: Thirty-fourRyR2-positive CPVT patients with...
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