Article
Successful treatment with cladribine of Erdheim-Chester disease with orbital and central nervous system involvement developing after treatment of Langerhans cell histiocytosis.
Vojnosanitetski pregled - 1 Jan 2016
Perić Predrag, Antić Branislav, Knezević-Usaj Slavica, Radić-Tasić Olga, Radovinović-Tasić Sanja, Vasić-Vilić Jasenka, Sekulović Leposava, Tarabar Olivera, Tukić Ljiljana, Jovandić Stevo, Magić Zvonko
Abstract excerpt
INTRODUCTION: Erdheim-Chester disease (ECD) is a rare, systemic form of non-Langerhans cell histiocytosis of the juvenile xanthogranuloma family with characteristic bilateral symmetrical long bone osteosclerosis, associated with xanthogranulomatous extra skeletal organ involvement. In ECD, central nervous system (CNS) and orbital lesions are frequent, and more than half of ECD pa tients carry the V600E mutation...
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