Article
Clinical manifestations and management of life-threatening bleeding in the largest group of patients with severe factor XIII deficiency.
International journal of hematology - 1 Nov 2014
Naderi Majid, Dorgalaleh Akbar, Alizadeh Shaban, Tabibian Shadi, Hosseini Soudabeh, Shamsizadeh Morteza, Bamedi Taregh
Abstract excerpt
Factor XIII (FXIII) deficiency is a rare hemorrhagic disorder for which the highest incidence occurs in southeast Iran. The aim of this study was to assess molecular characteristics, clinical manifestations and management of life-threatening diathesis in FXIII deficiency. This study was conducted on 190 patients with FXIII deficiency. Genotype analysis for the most frequent mutation of FXIII-A subunit gene in...
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