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Article

Batten disease is linked to altered expression of mitochondria-related metabolic molecules.

Neurochemistry international - 1 Jun 2013

Kang Sunyang, Seo Jae Hong, Heo Tae-Hwe, Kim Sung-Jo

Abstract excerpt

Batten disease (BD)--also known as juvenile neuronal ceroid lipofuscinoses-is an inherited neurodegenerative disorder caused by CLN3 gene mutations. Although CLN3-related oxidative and mitochondrial stresses have been studied in BD, the pathologic mechanism of the disease is not clearly understood. To address the molecular factors linked to high levels of oxidative stress in BD, we examined the expression of...

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Source

Identifiers

PMID: 23524239
DOI: 10.1016/j.neuint.2013.03.007

Genes

CLN3

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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