Article
Alloantibodies against the B subunit of plasma factor XIII developed in its congenital deficiency.
Thrombosis and haemostasis - 1 Apr 2013
Wada Hideho, Souri Masayoshi, Matsumoto Rui, Sugihara Takashi, Ichinose Akitada
Abstract excerpt
Factor XIII (FXIII) is a fibrin-stabilising factor consisting of catalytic A subunits (FXIII-A) and carrier B subunits (FXIII-B). FXIII-B prevents the fast clearance of FXIII-A from the circulation. Congenital FXIII-A deficiency is a rare bleeding disorder, and congenital FXIII-B deficiency is even rarer. Through our recent nationwide survey on "acquired haemophilia-like disease due to anti-FXIII autoantibodies,"...
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