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Article

Inherited hematological disorders due to defects in coat protein (COP)II complex.

American journal of hematology - 1 Feb 2013

Russo Roberta, Esposito Maria Rosaria, Iolascon Achille

Abstract excerpt

Many diseases attributed to trafficking defects are primary disorders of protein folding and assembly. However, an increasing number of disease states are directly attributable to defects in trafficking machinery. In this context, the cytoplasmic coat protein (COP)II complex plays a pivotal role: it mediates the anterograde transport of correctly folded secretory cargo from the endoplasmic reticulum towards the...

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Identifiers

PMID: 22764119
DOI: 10.1002/ajh.23292

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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Inherited hematological disorders due to defects in coat protein (COP)II complex.PMID 22764119Read ↗

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