Article
Pulmonary alveolar proteinosis.
European respiratory review : an official journal of the European Respiratory Society - 1 Jun 2011
Borie R, Danel C, Debray M-P, Taille C, Dombret M-C, Aubier M, Epaud R, Crestani B
Abstract excerpt
Pulmonary alveolar proteinosis (PAP) is a rare pulmonary disease characterised by alveolar accumulation of surfactant. It may result from mutations in surfactant proteins or granulocyte macrophage-colony stimulating factor (GM-CSF) receptor genes, it may be secondary to toxic inhalation or haematological disorders, or it may be auto-immune, with anti-GM-CSF antibodies blocking activation of alveolar macrophages....
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