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Article

Profound left ventricular remodeling associated with LAMP2 cardiomyopathy.

The American journal of cardiology - 15 Oct 2010

Maron Barry J, Roberts William C, Ho Carolyn Y, Kitner Carrie, Haas Tammy S, Wright Gregory B, Moazami Nader, Feldman David S

Abstract excerpt

Lysosome-associated membrane protein (LAMP2) cardiomyopathy is an X-linked and highly progressive myocardial storage disorder associated with diminished survival, which clinically resembles sarcomeric hypertrophic cardiomyopathy. As shown here in a young woman, the natural history of LAMP2 may demonstrate an extreme profile of left ventricular remodeling with regression of hypertrophy (i.e. marked wall thinning),...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Source

Identifiers

PMID: 20920663
DOI: 10.1016/j.amjcard.2010.06.035

Genes

LAMP2

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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