Article
Pulmonary embolism after snake bite in a child with Diamond-Blackfan anemia.
Journal of pediatric hematology/oncology - 1 Jan 2011
Makis Alexandros, Kattamis Antonis, Grammeniatis Vassilios, Sihlimiri Polyxeni, Kotsonis Haralambos, Iliadis Andreas, Siamopoulou Antigone, Chaliasos Nikolaos
Abstract excerpt
Diamond-Blackfan anemia (DBA) is a rare, congenital, pure red blood cell aplasia owing to gene defects affecting the function of ribosomal proteins, essential for erythroid maturation. Iron overload is a serious complication of chronic transfusions, which may lead to cardiac toxicity and endothelial damage. We report a case of pulmonary embolism, observed after viper bite in a transfusion-dependent child with DBA...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.
