Article
Recurrence of bile salt export pump deficiency after liver transplantation.
The New England journal of medicine - 1 Oct 2009
Jara Paloma, Hierro Loreto, Martínez-Fernández Pilar, Alvarez-Doforno Rita, Yánez Francisca, Diaz María C, Camarena Carmen, De la Vega Angela, Frauca Esteban, Muñoz-Bartolo Gema, López-Santamaría Manuel, Larrauri Javier, Alvarez Luis
Abstract excerpt
Severe bile salt export pump (BSEP) deficiency is a hereditary cholestatic condition that starts in infancy and leads to end-stage liver disease. Three children who underwent orthotopic liver transplantation for severe BSEP deficiency had post-transplantation episodes of cholestatic dysfunction that mimicked the original disease. Remission of all episodes was achieved by intensifying the immunosuppressive...
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