Article
Alpha-1-antitrypsin deficiency panniculitis.
Dermatologic clinics - 1 Oct 2008
Valverde Ricardo, Rosales Belén, Ortiz-de Frutos Francisco Javier, Rodríguez-Peralto José Luis, Ortiz-Romero Pablo L
Abstract excerpt
Alpha-1-antitrypsin deficiency is a congenital error of metabolism linked to pulmonary (emphysema) and liver (cirrhosis) disease. Since 1972, panniculitis has been associated with this deficiency, initially related to Weber-Christian syndrome and finally as a differentiated entity. Clinical manif...
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