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Article

Alpha-1-antitrypsin deficiency panniculitis.

Dermatologic clinics - 1 Oct 2008

Valverde Ricardo, Rosales Belén, Ortiz-de Frutos Francisco Javier, Rodríguez-Peralto José Luis, Ortiz-Romero Pablo L

Abstract excerpt

Alpha-1-antitrypsin deficiency is a congenital error of metabolism linked to pulmonary (emphysema) and liver (cirrhosis) disease. Since 1972, panniculitis has been associated with this deficiency, initially related to Weber-Christian syndrome and finally as a differentiated entity. Clinical manifestations typically consist of wide nodular lesions on the trunk and proximal extremities that evolve to ulceration and...

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Identifiers

PMID: 18793976
DOI: 10.1016/j.det.2008.05.001

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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