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Article

Defect in fatty acid esterification of dolichol in Niemann-Pick type C1 mouse livers in vivo.

Biochimica et biophysica acta - 1 Apr 2007

Turunen Mikael, Schedin-Weiss Sophia

Abstract excerpt

Fatty acid esterification of dolichol and cholesterol in Niemann-Pick type C1 mouse (Balb/c NIH npc1(-/-)) livers was investigated in response to treatment with peroxisomal proliferators. These inducers have hypolipidemic properties and influence the mevalonate pathway and the intracellular transport of the final products of this biosynthetic route. Such inducers are consequently interesting to use in a disease...

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Source

Identifiers

PMID: 17292665
DOI: 10.1016/j.bbalip.2007.01.002

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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