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Article

Regional and cellular neuropathology in the palmitoyl protein thioesterase-1 null mutant mouse model of infantile neuronal ceroid lipofuscinosis

10 Apr 2004

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PMID: 15193291
DOI: 10.1016/j.nbd.2004.02.010

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Related research

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Regional and cellular neuropathology in the palmitoyl protein thioesterase-1 null mutant mouse model of infantile neuronal ceroid lipofuscinosisPMID 15193291Read ↗

Adult neuronal ceroid lipofuscinosis caused by deficiency in palmitoyl protein thioesterase 1.Semantic proximity Read ↗

cDNA and Genomic Cloning of Human Palmitoyl-Protein Thioesterase (PPT), the Enzyme Defective in Infantile Neuronal Ceroid LipofuscinosisSemantic proximity Read ↗

Mouse models of neuronal ceroid lipofuscinoses: Useful pre-clinical tools to delineate disease pathophysiology and validate therapeuticsSemantic proximity Read ↗

The Role of Attenuated Astrocyte Activation in Infantile Neuronal Ceroid LipofuscinosisSemantic proximity Read ↗

Mutations in the palmitoyl protein thioesterase gene causing infantile neuronal ceroid lipofuscinosis.Semantic proximity Read ↗

Proteomics insights into infantile neuronal ceroid lipofuscinosis (CLN1) point to the involvement of cilia pathology in the disease.Semantic proximity Read ↗

Sex- and region-biased depletion of microglia/macrophages attenuates CLN1 disease in miceSemantic proximity Read ↗

NMDA Receptor Dysregulation by Defective Depalmitoylation in the Infantile Neuronal Ceroid Lipofuscinosis Mouse ModelSemantic proximity Read ↗

Immune cells perturb axons and impair neuronal survival in a mouse model of infantile neuronal ceroid lipofuscinosis.Semantic proximity Read ↗

Palmitoyl protein thioesterase (PPT) localizes into synaptosomes and synaptic vesicles in neurons: implications for infantile neuronal ceroid lipofuscinosis (INCL).Semantic proximity Read ↗

Decreased sensitivity of palmitoyl protein thioesterase 1-deficient neurons to chemical anoxia.Semantic proximity Read ↗

Infantile neuronal ceroid lipofuscinosis: no longer just a 'Finnish' disease.Semantic proximity Read ↗

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