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Article

Clinical and genetic studies of familial hemophagocytic lymphohistiocytosis in Oman: need for early treatment.

Pediatric hematology and oncology - 1 Dec 2003

Al-Lamki Zakia, Wali Yasser A, Pathare Anil, Ericson Kim Göransdotter, Henter Jan-Inge

Abstract excerpt

Hemophagocytic lymphohistiocytosis (HLH) embraces the frequently indistinguishable conditions of familial hemophagocytic lymphohistiocytosis (FHL) and virus-associated hemophagocytic syndrome (VAHS). Without therapy FHL is invariably fatal, but successful therapy, including chemotherapy and immunotherapy followed by bone marrow transplantation (BMT), has been presented. To clarify the outcome of HLH in a...

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PMID: 14578030

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

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