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Article

Inherited complete factor I deficiency associated with systemic lupus erythematosus, higher susceptibility to infection and low levels of factor H.

Scandinavian journal of immunology - 1 Jun 2001

Amadei N, Baracho G V, Nudelman V, Bastos W, Florido M P, Isaac L

Abstract excerpt

Here we describe two new cases of complete deficiency of factor I (fI) in two sisters from a consanguineous Brazilian family. The eldest sibling (20-year-old) developed systemic lupus erythematosus (SLE) early during childhood while the youngest had been committed on several occasions owing to repeated infections although she was asymptomatic for auto-immune diseases. We also detected lower concentrations of C3...

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Identifiers

PMID: 11422911
DOI: 10.1046/j.1365-3083.2001.00931.x

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

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