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Article

Recent progress in lysosomal alpha-mannosidase and its deficiency.

Experimental & molecular medicine - 31 Mar 2001

Sun H, Wolfe J H

Abstract excerpt

Lysosomal alpha-mannosidase (EC 3.2.1.24) is a major exoglycosidase in the glycoprotein degradation pathway. A deficiency of this enzyme causes the lysosomal storage disease, alpha-mannosidosis, which has been described in humans, cattle, domestic cats and guinea pigs. Recently, great progress has been made in studying the enzyme and its deficiency. This includes cloning of the gene encoding the enzyme,...

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Identifiers

PMID: 11322479
DOI: 10.1038/emm.2001.1

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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