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Article

Importance of dural ectasia in phenotypic assessment of Marfan's syndrome.

Lancet (London, England) - 11 Sept 1999

Fattori R, Nienaber C A, Descovich B, Ambrosetto P, Reggiani L B, Pepe G, Kaufmann U, Negrini E, von Kodolitsch Y, Gensini G F

Abstract excerpt

BACKGROUND: Early identification of Marfan's syndrome is fundamental in the prevention of aortic dilatation, but the wide phenotypic expression of the disorder makes the clinical diagnosis very difficult. Dural ectasia has been classified as a major diagnostic criterion; however, its prevalence is not known. We aimed to identify the true prevalence of dural ectasia in Marfan's syndrome, and to investigate its...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Source

Identifiers

PMID: 10489951
DOI: 10.1016/s0140-6736(98)12448-0

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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