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Article

Normal cochlear function in mdx and mdx(Cv3) Duchenne muscular dystrophy mouse models.

The Laryngoscope - 1 Aug 1999

Pillers D A, Duncan N M, Dwinnell S J, Rash S M, Kempton J B, Trune D R

Abstract excerpt

OBJECTIVES/HYPOTHESIS: Sensorineural hearing loss has been found in association with inherited muscular dystrophies in humans and in mouse models. An increased brainstem auditory evoked response threshold has been previously reported in the dystrophin-deficient mdx mouse model for Duchenne muscular dystrophy, suggesting that full-length dystrophin (Dp427) is involved in hearing. The objective of the present study...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Source

Identifiers

PMID: 10443839
DOI: 10.1097/00005537-199908000-00023

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ABR

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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