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Article

Hyperinsulinaemic hypoglycaemia associated with persistent hyperammonaemia.

European journal of pediatrics - 1 May 1999

Kitaura J, Miki Y, Kato H, Sakakihara Y, Yanagisawa M

Abstract excerpt

UNLABELLED: Two cases of hyperinsulinaemic hypoglycaemia associated with persistent hyperammonaemia in unrelated infants of 7 days and 4 months of age are reported. Blood ammonia levels were 100-300 micromol/l (normal values <40 micromol/l). The hyperammonaemia was asymptomatic and not associated with any of the abnormalities of amino acids or organic acids observed in urea cycle enzyme defects. Orotic aciduria...

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Source

Identifiers

PMID: 10333126
DOI: 10.1007/s004310051103

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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