Article

DADA2 presenting as nonimmune hemolytic anemia with recurrent macrophage activation syndrome

2024-01-31

Abstract excerpt

Hemolytic anemia is a common clinical problem with diverse etiology. 10-year-old boy presented with severe pallor. He had hemolytic facies, hepatosplenomegaly & deformity of small joints. Investigations revealed DAT-ve anemia, reticulocytosis and low haptoglobin. BM showed erythroid hyperplasia. Past history revealed recurrent fever, rash, hepatosplenomegaly, lymphadenopathy and poly arthritis diagnosed as systemi...

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Literature Corpus work: f2f027e8-c0e0-59e3-b25d-4e09a1b8cf45
DOI: 10.22541/au.170666917.71715504/v1

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