Article

Multiple Breath Washout in Primary Ciliary Dyskinesia: Potential for Lung Disease Monitoring

2025-06-11

Abstract excerpt

Primary ciliary dyskinesia (PCD) is a heterogeneous genetic disorder characterized by structural and functional abnormalities of motile cilia, leading to chronic oto-sino-pulmonary symptoms and progressive lung damage. Markers of early lung disease in PCD may help to identify individuals who may benefit from closer monitoring or earlier, more aggressive interventions. Multiple Breath Washout (MBW) offers a noninva...

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Literature Corpus work: 749bed11-283d-5f0c-a429-5c75a9aec509
DOI: 10.22541/au.174961444.45740793/v1

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