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Article

MRI based semi-quantitative scoring system analysis of thigh muscles in patients with VCP disease

2023-10-17

Abstract excerpt

Inclusion body myopathy with Paget’s disease and frontotemporal dementia (IBMPFD) or VCP disease or multisystem proteinopathy-1 (MSP1), is a rare disease caused by mutations in the valosin-containing protein ( VCP ) gene that commonly manifests as proximal myopathy. We investigated the value of a 5-grade semi-quantitative scoring system based on MRI for studying myopathy progression in VCP disease. Among the subje...

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Identifiers and source

Literature Corpus work
614537fe-053e-5c22-ada7-8d1a0d1acdb7
DOI
10.21203/rs.3.rs-3443700/v1
Open publication

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MRI based semi-quantitative scoring system analysis of thigh muscles in patients with VCP diseaseDOI 10.21203/rs.3.rs-3443700/v1
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