Article

Von Hippel–Lindau syndrome with multiple neuroendocrine neoplasms as the initial manifestation - a case report of an elusive presentation

2023-03-28

Abstract excerpt

<h4>Background: </h4> Von Hippel–Lindau (VHL) syndrome is a rare genetic tumor characterized by the recurrent development of multiple benign or malignant tumors involving multiple organs throughout a patient’s life. It is easy to precisely diagnose when the patient has characteristic central nervous system hemangioblastomas (CNS-H) as the main manifestation.VHL disease can be classified into type 1,2A,2B, and 2C b...

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Literature Corpus work: 47caba2d-f7f0-585d-aa41-089d28d97591
DOI: 10.21203/rs.3.rs-2739711/v1

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