Article

Clinical and molecular basis of hepatocerebral mitochondrial DNA depletion syndrome in Japan: Evaluation of outcomes after liver transplantation

2020-06-11

Abstract excerpt

<title>Abstract</title> <p><bold>Background </bold>Hepatocerebral mitochondrial DNA depletion syndrome (MTDPS) is a disease caused by defects in mitochondrial DNA maintenance and leads to liver failure and neurological complications during infancy. Liver transplantation (LT) remains controversial due to poor outcomes associated with extrahepatic symptoms. The purposes of this study were to clarify the current cli...

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Literature Corpus work: 277b83d6-30c6-5dbc-b8af-dd2bfa3ab3d7
DOI: 10.21203/rs.3.rs-17666/v2

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