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Article

Hereditary dysphasic disinhibition dementia A frontotemporal dementia linked to 17 q21‐‐22

1 Jun 1998

Abstract excerpt

OBJECTIVE: The clinical and pathologic features of hereditary dysphasic disinhibition dementia (HDDD) are described to determine whether it is a variant of known dementias. BACKGROUND: Several dementing disorders have clinical and pathologic similarities with AD, Pick's disease, and the "nonspecific" dementias. A detailed description of clinical and pathologic presentation will aid classification, but ultimately...

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PMID: 9633693
DOI: 10.1212/wnl.50.6.1546

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