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Article

Endolymphatic sac tumors. A source of morbid hearing loss in von Hippel-Lindau disease.

JAMA - 14 May 1997

Manski T J, Heffner D K, Glenn G M, Patronas N J, Pikus A T, Katz D, Lebovics R, Sledjeski K, Choyke P L, Zbar B, Linehan W M, Oldfield E H

Abstract excerpt

OBJECTIVES: Isolated reports suggest a possible association of endolymphatic sac tumors (ELSTs), which are extremely rare in the general population, with von Hippel-Lindau disease (VHL). To determine if hearing loss and ELSTs are a component of VHL, we examined prevalence, clinical presentation, and natural history of hearing loss and ELSTs in VHL. DESIGN: Brain magnetic resonance images (MRIs) from 374 patients...

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Identifiers

PMID: 9145719
DOI: 10.1001/jama.277.18.1461

Genes

VHL

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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