Article
Hepatobiliary disease in cystic fibrosis patients with pancreatic sufficiency.
Hepatology (Baltimore, Md.) - 1 Apr 1995
Waters D L, Dorney S F, Gruca M A, Martin H C, Howman-Giles R, Kan A E, De Silva M, Gaskin K J
Abstract excerpt
Focal and multilobular biliary cirrhosis are considered pathognomonic of cystic fibrosis (CF) and almost invariably have been reported in patients with steatorrhea. In contrast, patients with pancreatic sufficiency and normal absorption are considered less likely to develop liver or biliary tract...
Topics
- Biliary Tract Diseases
- Child
- Cystic Fibrosis
- Cystic Fibrosis Transmembrane Conductance Regulator
- Female
- Humans
- Liver Cirrhosis
- Male
- Membrane Proteins
- Mutation
- Pancreas