Successful Anesthetic Management of Deceased Donor Liver Transplant in a Patient With Neonatal Sclerosing Cholangitis As a Result of DCDC2 (doublecortin domain-containing protein 2) Mutation: A Case Report.

Abstract excerpt

Neonatal sclerosing cholangitis, which develops due to mutations in doublecortin domain -containing protein 2, is a rare and serious autosomal recessive inherited end -stage liver disease and frequently requires liver transplant due to decompensated biliary cirrhosis in childhood. Here, we present the anesthetic management of a deceased donor liver transplant in an 8y -ear -old female patient with hepatopulmonary...

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